This course focuses on understanding the underlying biochemical and genetic basis of inborn errors of metabolism, as well as the nutritional management strategies required to optimize the health and well-being of affected individuals. This course covers diseases including phenylketonuria, maple syrup urine disease, galactosemic, Glycogen storage disease, homocystinuria, Medium-chain Acyl-CoA Dehydrogenase (MCAD) deficiency and familial hypercholesterolemia.